Saburo Kishimoto, Mari Yamamoto, Tomoko Nomiyama, Kiyomi Kawa, Hideya Takenaka, Kouji Tukitani
DOI: 10.1080/000155501750376311

This study reports on the clinical and light microscopic features of a nevoid basal cell carcinoma syndrome with the complication of eosinophilic pustular folliculitis. To the authors' knowledge, this is the first report of such an association, which is possibly due to immune dysregulation. Moreover, the patient experienced remission of eosinophilic pustular folliculitis after removal of the jaw cyst. One possible explanation for the remission is that a long-lasting TH1 type inflammatory response as a result of the bone defect produces effective cytokines such as interferon- γ .